Lymphangioma of the esophagus is a benign vascular tumor that rarely occurs in the upper gastrointestinal tract. We report a rare case of lymphangioma of the esophagus and our experience with endoscopic resection of this lesion. Lymphangiomas are benign lesions that arise from the cystic dilatation of hamartomas in deep lymphatic tissue and are rarely found in the GI tract (1%). The esophagus is the most unusual location for this lesion. The diagnosis of lymphagioma is usually made on histopathology. The masses are composed of enlarged channels lined by lymphatic endothelial cells surrounded by a loose myxoid stroma. Standard biopsies are often normal as the lesions are submucosal. The treatment of esophageal lymphangioma is conservative in asymptomatic patients. For symptomatic pateints, response to surgical or endoscopic removal of these tumors is excellent. However, a large tumor with symptoms or a lesion suspicious for malignancy requires surgical resection. Conclusion: Lymphangioma of the esophagus is a rare submucosal tumor, generally small and benign in nature. Endoscopic ultrasound is an excellent tool for diagnosis of these lesions. Our experience reaffirms that endoscopic excision of such lesions is safe and appears to be without major complications.